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Klippel-Trenaunay-Weber Syndrome Complicated by Extrafetal Umbilical Vein VarixLoma Linda University Medical Center
Loma Linda University Medical Center Klippel-Trenaunay-Weber (KTW) syndrome is arare vascular malformation including soft-tissue hypertrophy,varicose veins, cutaneous hemangiomas,and arteriovenous fistulas. The majority of reportedcases were discovered at birth; only 7 cases havebeen reported in utero. Varicosities of the umbilicalvein in utero involving the extra fetal portion of thecord are rare. Thrombosis of these varicies often resultsin the death of the fetus. No articles, at thistime, report a case of KTW associated with an umbilicalvarix and subsequent thrombosis. The followingcase describes the sonographic appearanceof both these abnormalities.
Key Words: Klippel-Trenaunay-Weber umbilical vein varix
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